(Q38261844)

1 September 2017

1 reference

title

Polyglutamine Aggregation in Huntington Disease: Does Structure Determine Toxicity? (English)

1 reference

1 September 2017

0 references

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25336039%20AND%20SRC:MED&resulttype=core&format=json

6 June 2020

Philippe Djian

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25336039%20AND%20SRC:MED&resulttype=core&format=json

6 June 2020

author name string

Guylaine Hoffner

series ordinal

1

1 reference

1 September 2017

Philippe Djian

series ordinal

2

1 reference

1 September 2017

22 October 2014

1 reference

1 September 2017

Molecular Neurobiology

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25336039%20AND%20SRC:MED&resulttype=core&format=json

6 June 2020

volume

52

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25336039%20AND%20SRC:MED&resulttype=core&format=json

6 June 2020

issue

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25336039%20AND%20SRC:MED&resulttype=core&format=json

6 June 2020

page(s)

1297-1314

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:25336039%20AND%20SRC:MED&resulttype=core&format=json

https://scigraph.springernature.com/pub.10.1007/s12035-014-8932-1

6 June 2020

exact match

0 references

cites work

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Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

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Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain

21 January 2018

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Huntingtin acts in the nucleus to induce apoptosis but death does not correlate with the formation of intranuclear inclusions.

21 January 2018

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Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal death

21 January 2018

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21 January 2018

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Huntington's disease intranuclear inclusions contain truncated, ubiquitinated huntingtin protein

21 January 2018

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Oligomeric and polymeric aggregates formed by proteins containing expanded polyglutamine

21 January 2018

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Purification of neuronal inclusions of patients with Huntington's disease reveals a broad range of N-terminal fragments of expanded huntingtin and insoluble polymers

21 January 2018

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Proteases acting on mutant huntingtin generate cleaved products that differentially build up cytoplasmic and nuclear inclusions

21 January 2018

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Huntingtin forms toxic NH2-terminal fragment complexes that are promoted by the age-dependent decrease in proteasome activity.

21 January 2018

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Cleavage of huntingtin by apopain, a proapoptotic cysteine protease, is modulated by the polyglutamine tract

21 January 2018

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Caspase 3-cleaved N-terminal fragments of wild-type and mutant huntingtin are present in normal and Huntington's disease brains, associate with membranes, and undergo calpain-dependent proteolysis.

21 January 2018

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Perturbation with intrabodies reveals that calpain cleavage is required for degradation of huntingtin exon 1

21 January 2018

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Aberrant splicing of HTT generates the pathogenic exon 1 protein in Huntington disease

21 January 2018

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Long glutamine tracts cause nuclear localization of a novel form of huntingtin in medium spiny striatal neurons in HdhQ92 and HdhQ111 knock-in mice

21 January 2018

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Truncated N-terminal fragments of huntingtin with expanded glutamine repeats form nuclear and cytoplasmic aggregates in cell culture.

21 January 2018

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Polyglutamine expansion of huntingtin impairs its nuclear export

21 January 2018

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Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Paradoxical delay in the onset of disease caused by super-long CAG repeat expansions in R6/2 mice.

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

CAG repeat lengths > or =335 attenuate the phenotype in the R6/2 Huntington's disease transgenic mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Preferential accumulation of N-terminal mutant huntingtin in the nuclei of striatal neurons is regulated by phosphorylation

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Transcriptional abnormalities in Huntington disease

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Length of huntingtin and its polyglutamine tract influences localization and frequency of intracellular aggregates

21 January 2018

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Accumulation of N-terminal mutant huntingtin in mouse and monkey models implicated as a pathogenic mechanism in Huntington's disease.

21 January 2018

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Reprogramming Huntington monkey skin cells into pluripotent stem cells

21 January 2018

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Induced pluripotent stem cell lines from Huntington's disease mice undergo neuronal differentiation while showing alterations in the lysosomal pathway

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The first reported generation of several induced pluripotent stem cell lines from homozygous and heterozygous Huntington's disease patients demonstrates mutation related enhanced lysosomal activity

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Induced pluripotent stem cells from patients with Huntington's disease show CAG-repeat-expansion-associated phenotypes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Astrocytes generated from patient induced pluripotent stem cells recapitulate features of Huntington's disease patient cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Huntingtin-encoded polyglutamine expansions form amyloid-like protein aggregates in vitro and in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Intra- and intermolecular beta-pleated sheet formation in glutamine-repeat inserted myoglobin as a model for polyglutamine diseases

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Amyloid-like features of polyglutamine aggregates and their assembly kinetics

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Polyglutamine expansion as a pathological epitope in Huntington's disease and four dominant cerebellar ataxias

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Amyloid formation by mutant huntingtin: threshold, progressivity and recruitment of normal polyglutamine proteins

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

A linear lattice model for polyglutamine in CAG-expansion diseases

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The structure of a polyQ-anti-polyQ complex reveals binding according to a linear lattice model

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Linear and extended: a common polyglutamine conformation recognized by the three antibodies MW1, 1C2 and 3B5H10

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Disease-Associated Polyglutamine Stretches in Monomeric Huntingtin Adopt a Compact Structure

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Solution structure of polyglutamine tracts in GST-polyglutamine fusion proteins

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Secondary Structure of Huntingtin Amino-Terminal Region

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Cause of neural death in neurodegenerative diseases attributable to expansion of glutamine repeats

21 January 2018

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Amyloid fibril protein nomenclature: 2012 recommendations from the Nomenclature Committee of the International Society of Amyloidosis

21 January 2018

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Amyloid-like inclusions in Huntington's disease.

21 January 2018

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The X-ray interpretation of denaturation and the structure of the seed globulins

21 January 2018

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Molecular structures of amyloid and prion fibrils: consensus versus controversy

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Amyloid fibers are water-filled nanotubes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Dual binding modes of Congo red to amyloid protofibril surface observed in molecular dynamics simulations

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Congo red and protein aggregation in neurodegenerative diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The amyloid-Congo red interface at atomic resolution

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Quantitative evaluation of congo red binding to amyloid-like proteins with a beta-pleated sheet conformation

21 January 2018

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https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

A model for structure-dependent binding of Congo red to Alzheimer beta-amyloid fibrils.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The Huntington's disease protein interacts with p53 and CREB-binding protein and represses transcription

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Identities of sequestered proteins in aggregates from cells with induced polyglutamine expression

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Differential morphology and composition of inclusions in the R6/2 mouse and PC12 cell models of Huntington's disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Transglutaminase-catalyzed crosslinking in neurological disease: from experimental evidence to therapeutic inhibition.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Inhibition of huntingtin fibrillogenesis by specific antibodies and small molecules: implications for Huntington's disease therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Huntingtin spheroids and protofibrils as precursors in polyglutamine fibrilization

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

A cell-based assay for aggregation inhibitors as therapeutics of polyglutamine-repeat disease and validation in Drosophila

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Inhibition of polyglutamine aggregation in R6/2 HD brain slices-complex dose-response profiles

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Propagating structure of Alzheimer's beta-amyloid(10-35) is parallel beta-sheet with residues in exact register

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Antiparallel -sheet architecture in Iowa-mutant -amyloid fibrils

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

New model for crystalline polyglutamine assemblies and their connection with amyloid fibrils

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Structural characterization of polyglutamine fibrils by solid-state NMR spectroscopy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The aggregation-enhancing huntingtin N-terminus is helical in amyloid fibrils

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Mutational analysis of the structural organization of polyglutamine aggregates

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

A compact beta model of huntingtin toxicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

A structure-based analysis of huntingtin mutant polyglutamine aggregation and toxicity: evidence for a compact beta-sheet structure.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

An expanded glutamine repeat destabilizes native ataxin-3 structure and mediates formation of parallel beta -fibrils.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Soluble polyglutamine oligomers formed prior to inclusion body formation are cytotoxic

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Structure of inclusions of Huntington's disease brain revealed by synchrotron infrared microspectroscopy: polymorphism and relevance to cytotoxicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Models of amyloid seeding in Alzheimer's disease and scrapie: mechanistic truths and physiological consequences of the time-dependent solubility of amyloid proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Physical chemistry of polyglutamine: intriguing tales of a monotonous sequence

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

A one-hit model of cell death in inherited neuronal degenerations

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Huntington's disease age-of-onset linked to polyglutamine aggregation nucleation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Critical nucleus size for disease-related polyglutamine aggregation is repeat-length dependent

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Protein misfolding detected early in pathogenesis of transgenic mouse model of Huntington disease using amyloid seeding assay

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Aging causes distinct characteristics of polyglutamine amyloids in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Distinct conformations of in vitro and in vivo amyloids of huntingtin-exon1 show different cytotoxicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Cross-seeding fibrillation of Q/N-rich proteins offers new pathomechanism of polyglutamine diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The first 17 amino acids of Huntingtin modulate its sub-cellular localization, aggregation and effects on calcium homeostasis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Flanking sequences profoundly alter polyglutamine toxicity in yeast

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Oligoproline effects on polyglutamine conformation and aggregation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Critical role of the proline-rich region in Huntingtin for aggregation and cytotoxicity in yeast.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

In-cell aggregation of a polyglutamine-containing chimera is a multistep process initiated by the flanking sequence

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Mutant huntingtin N-terminal fragments of specific size mediate aggregation and toxicity in neuronal cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The chaperonin TRiC blocks a huntingtin sequence element that promotes the conformational switch to aggregation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Polyglutamine disruption of the huntingtin exon 1 N terminus triggers a complex aggregation mechanism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Reconsidering the mechanism of polyglutamine peptide aggregation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Slow amyloid nucleation via α-helix-rich oligomeric intermediates in short polyglutamine-containing huntingtin fragments.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Inhibiting the nucleation of amyloid structure in a huntingtin fragment by targeting α-helix-rich oligomeric intermediates

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The chaperonin TRiC controls polyglutamine aggregation and toxicity through subunit-specific interactions

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Protein folding: sticky N17 speeds huntingtin pile-up

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Essential role of coiled coils for aggregation and activity of Q/N-rich prions and PolyQ proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Mutant huntingtin fragments form oligomers in a polyglutamine length-dependent manner in vitro and in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Post-translational modifications of expanded polyglutamine proteins: impact on neurotoxicity.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Small changes, big impact: posttranslational modifications and function of huntingtin in Huntington disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Parkin facilitates the elimination of expanded polyglutamine proteins and leads to preservation of proteasome function.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

SUMO modification of Huntingtin and Huntington's disease pathology

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

IKK phosphorylates Huntingtin and targets it for degradation by the proteasome and lysosome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Full-length human mutant huntingtin with a stable polyglutamine repeat can elicit progressive and selective neuropathogenesis in BACHD mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Serines 13 and 16 are critical determinants of full-length human mutant huntingtin induced disease pathogenesis in HD mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Serine phosphorylation suppresses huntingtin amyloid accumulation by altering protein aggregation properties.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Kinase inhibitors modulate huntingtin cell localization and toxicity.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The chaperone-like protein HYPK acts together with NatA in cotranslational N-terminal acetylation and prevention of Huntingtin aggregation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Mechanism of cis-inhibition of polyQ fibrillation by polyP: PPII oligomers and the hydrophobic effect

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Polyglutamine induced misfolding of huntingtin exon1 is modulated by the flanking sequences

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Soluble androgen receptor oligomers underlie pathology in a mouse model of spinobulbar muscular atrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Monoclonal antibodies recognize distinct conformational epitopes formed by polyglutamine in a mutant huntingtin fragment

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Hsp70 and Hsp40 attenuate formation of spherical and annular polyglutamine oligomers by partitioning monomer

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Detection of polyglutamine protein oligomers in cells by fluorescence correlation spectroscopy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Tracking mutant huntingtin aggregation kinetics in cells reveals three major populations that include an invariant oligomer pool.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Identification of novel potentially toxic oligomers formed in vitro from mammalian-derived expanded huntingtin exon-1 protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Identical oligomeric and fibrillar structures captured from the brains of R6/2 and knock-in mouse models of Huntington's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

TR-FRET-based duplex immunoassay reveals an inverse correlation of soluble and aggregated mutant huntingtin in huntington's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Fragments of HdhQ150 mutant huntingtin form a soluble oligomer pool that declines with aggregate deposition upon aging

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Transglutaminase action imitates Huntington's disease: selective polymerization of Huntingtin containing expanded polyglutamine.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Polyglutamine fibrillogenesis: the pathway unfolds

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Expansion of polyglutamine induces the formation of quasi-aggregate in the early stage of protein fibrillization

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Structural neurology: are seeds at the root of neuronal degeneration?

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Soluble pool of Abeta amyloid as a determinant of severity of neurodegeneration in Alzheimer's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Naturally secreted oligomers of amyloid beta protein potently inhibit hippocampal long-term potentiation in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Prevention of polyglutamine oligomerization and neurodegeneration by the peptide inhibitor QBP1 in Drosophila

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Inhibition of protein misfolding/aggregation using polyglutamine binding peptide QBP1 as a therapy for the polyglutamine diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Green tea (-)-epigallocatechin-gallate modulates early events in huntingtin misfolding and reduces toxicity in Huntington's disease models

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Absence of behavioral abnormalities and neurodegeneration in vivo despite widespread neuronal huntingtin inclusions

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Hsp70 and hsp40 chaperones can inhibit self-assembly of polyglutamine proteins into amyloid-like fibrils

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Protein structure by Fourier transform infrared spectroscopy: second derivative spectra

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

The use and misuse of FTIR spectroscopy in the determination of protein structure

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Infrared spectroscopy of proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

FTIR reveals structural differences between native beta-sheet proteins and amyloid fibrils.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

FT-IR approaches on amyloid fibril structure

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Pathogenic and Non-pathogenic Polyglutamine Tracts Have Similar Structural Properties: Towards a Length-dependent Toxicity Gradient

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

Inhibition of polyglutamine protein aggregation and cell death by novel peptides identified by phage display screening

21 January 2018

2 references

https://api.crossref.org/works/10.1007%2FS12035-014-8932-1

21 January 2018

12 December 2020

X-ray diffraction studies on amyloid filaments

1 reference

12 December 2020

Caspase cleavage of mutant huntingtin precedes neurodegeneration in Huntington's disease.

1 reference

12 December 2020

Polyglutamine homopolymers having 8-45 residues form slablike beta-crystallite assemblies

1 reference

12 December 2020

Calpain activation in Huntington's disease.

1 reference

12 December 2020

Neuropathological classification of Huntington's disease

1 reference

12 December 2020

[Optical polarization studies of amyloid substance]

1 reference

12 December 2020

Characterization of the Amyloid Fibril as a Cross- Protein

1 reference

12 December 2020

Sensitive biochemical aggregate detection reveals aggregation onset before symptom development in cellular and murine models of Huntington's disease

1 reference

12 December 2020

A toxic monomeric conformer of the polyglutamine protein

1 reference

12 December 2020